Atypical pulmonary artery sling with diffuse-type pulmonary arteriovenous fistula.
نویسندگان
چکیده
The case of a cyanotic infant with a rare combination of atypical pulmonary artery sling, imperforate anus, absence of the left kidney, interruption of the inferior vena cava, left side hemihypertrophy and diffuse-type pulmonary arteriovenous fistula is described. The clinical features were confusing, because of compounding abnormalities involving the respiratory tract and pulmonary circulation. The diagnostic approach to the etiology of cyanosis is discussed and the embryonic origin of pulmonary artery sling is reviewed.
منابع مشابه
Left pulmonary artery banding to repair ipsilateral diffuse pulmonary arteriovenous fistula
Congenital pulmonary arteriovenous fistula (PAVF) is a rare disease which causes hypoxemia by shunting deoxygenated blood from the pulmonary artery into pulmonary venous return. Lung transplantation is the most effective therapy to treat severe, diffuse PAVF. However, the availability of lungs for transplantation is limited in most parts in the world. For patients with diffuse PAVF affecting on...
متن کاملشیوع هیپرتانسیون پولمونر و عوامل مرتبط با آن در بیماران همودیالیزی
Background and purpose: Pulmonary hypertension (PH) has been reported in hemodialysis patients, but there are scant studies about its prevalence and mechanisms. The aim of this study was to determine the prevalence of pulmonary hypertension in hemodialysis patients and to study some of its possible etiologic factors. Materials and methods: Ïn this cross-sectional study, the prevalence of p...
متن کاملDiffuse Pulmonary Arteriovenous Malformation in Children: Essential Value of Contrast Echocardiography in Diagnosis
Pulmonary arteriovenous malformations (PAVM) are abnormal communications between pulmonary arteries and pulmonary veins, and most commonly congenital in nature. Although rare, it is an important consideration in cyanotic patients of unknown cause. We report 3 cases with diffuse PAVM in children with different clinical manifestations and initial diagnosis was made by transthoracic contrast echoc...
متن کاملPulmonary Arteriovenous Fistula: Clinical and Histologic Spectrum of Four Cases
Pulmonary arteriovenous fistula (PAVF) is abnormally dilated vessels that provide a right-to-left shunt between pulmonary artery and pulmonary vein and is clinically divided into simple and complex type. Here, we report four cases of surgically resected sporadic PAVFs presenting various clinical and histologic spectrums. Cases 1 (a 57-old-female) and 2 (a 54-old-female) presented as incidentall...
متن کاملUsefulness of dynamic volume scanning with 320-row CT in detecting recanalization of pulmonary arteriovenous fistula after coil embolization
Pulmonary arteriovenous fistula is a congenital and rarely acquired anomalous direct communications between pulmonary arteries and veins. Transcatheter embolization using metallic coil or detachable balloon is one of the common treatment procedure. However, recanalization after the embolization is one of the concern and its differentiation from the retrograde filling via pulmonary vein is diffi...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Journal of Korean Medical Science
دوره 14 شماره
صفحات -
تاریخ انتشار 1999